====== Sensorineural Hearing Loss ======
  * Ocular screening is recommended due to the frequent co-incidence of ocular disease 
  * Eye exam when first diagnosed and follow up as required. 
 
====Ocular/Visual Screening Recommendations====
  * Complete Eye Exam
  * Additional specialized testing based on findings

==== Ocular Associations ====
  * Anterior Segment Disease
    * Keratitis-ichthyosis-deafness syndrome
  * Posterior Segment Disease
    * [[usher_syndrome|Usher Syndrome]] 
    * Heridary Optic Neuropathies
      * [[leber_hereditary_optic_neuropathy|Leber Hereditary Optic Neuropathy]]
      * [[bilateral_optic_atrophy|Optic Atrophy]]
      * Wolfram Syndrome
    * Norrie Disease
    * Stickler Syndrome
    * [[marfan_syndrome|Marfan Syndrome]]
    * Heimler Syndrome
  * Anterior and Posterior Segment Disease
    * Cogan Syndrome
    * Congenital Rubella
    * Alport Syndrome
    * Waardenburg Syndrome


====== Resources ======
  * {{::ocular_manifestations_in_patients_with_sensineural_hearing_loss_2022.pdf |Zaheer HA et al. Ocular Manifestations in Patients with Sensorineural Hearing Loss. J Ophthalmic Vis Res 2002:17(4):551-573}}
  * {{::year_2019_jcih_position_statement.pdf |Principles and Guidelines for Early Hearing Detection and Intervention Programs. Joint Committee on Infant Hearing. 2019;4(2):1-44 see page 17 and 21}}

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