Table of Contents
Sensorineural Hearing Loss
Ocular/Visual Screening Recommendations
Ocular Associations
Resources
Sensorineural Hearing Loss
Ocular screening is recommended due to the frequent co-incidence of ocular disease
Eye exam when first diagnosed and follow up as required.
Ocular/Visual Screening Recommendations
Complete Eye Exam
Additional specialized testing based on findings
Ocular Associations
Anterior Segment Disease
Keratitis-ichthyosis-deafness syndrome
Posterior Segment Disease
Usher Syndrome
Heridary Optic Neuropathies
Leber Hereditary Optic Neuropathy
Optic Atrophy
Wolfram Syndrome
Norrie Disease
Stickler Syndrome
Marfan Syndrome
Heimler Syndrome
Anterior and Posterior Segment Disease
Cogan Syndrome
Congenital Rubella
Alport Syndrome
Waardenburg Syndrome
Resources
Zaheer HA et al. Ocular Manifestations in Patients with Sensorineural Hearing Loss. J Ophthalmic Vis Res 2002:17(4):551-573
Principles and Guidelines for Early Hearing Detection and Intervention Programs. Joint Committee on Infant Hearing. 2019;4(2):1-44 see page 17 and 21
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